{"id":1888456,"date":"2026-04-17T10:01:20","date_gmt":"2026-04-17T07:01:20","guid":{"rendered":"https:\/\/analyse.optim.biz\/?p=1888456"},"modified":"2026-04-17T10:01:20","modified_gmt":"2026-04-17T07:01:20","slug":"astazi-se-sarbatoreste-ziua-internationala-a-hemofiliei","status":"publish","type":"post","link":"https:\/\/analyse.optim.biz\/?p=1888456","title":{"rendered":"Ast\u0103zi se s\u0103rb\u0103tore\u0219te Ziua Interna\u021bional\u0103 a Hemofiliei"},"content":{"rendered":"<p>[analyse_image type=&#8221;featured&#8221; src=&#8221;https:\/\/blitz24.ro\/wp-content\/uploads\/2026\/04\/ziua-internationala-a-hemofiliei-scaled.jpg&#8221;]<\/p>\n<div class=\"cm-entry-summary\">\n<p><strong>Ziua Interna\u021bional\u0103 a Hemofiliei, s\u0103rb\u0103torit\u0103 ast\u0103zi, 17 aprilie, reprezint\u0103 o oportunitate important\u0103 de a cre\u0219te gradul de informare al popula\u021biei cu privire la diagnosticarea \u0219i tratamentul acestei afec\u021biuni, dar \u0219i de a atrage aten\u021bia autorit\u0103\u021bilor asupra necesit\u0103\u021bii \u00eembun\u0103t\u0103\u021birii accesului la servicii medicale.<\/strong><\/p>\n<p>De\u0219i hemofilia nu se vindec\u0103, tratamentul adecvat permite pacien\u021bilor s\u0103 duc\u0103 o via\u021b\u0103 activ\u0103 \u0219i s\u0103 se bucure de o bun\u0103 calitate a vie\u021bii.<\/p>\n<p>Tema stabilit\u0103 de Federa\u021bia Mondial\u0103 de Hemofilie pentru anul 2026 \u2014 \u201eDiagnosticarea: primul pas c\u0103tre tratament\u201d care \u00a0subliniaz\u0103 un adev\u0103r esen\u021bial: de\u0219i boala este prezent\u0103 de la na\u0219tere, ea este adesea descoperit\u0103 t\u00e2rziu.<\/p>\n<p><strong>Ce este hemofilia?<\/strong><\/p>\n<p>Hemofilia este o boal\u0103 genetic\u0103 rar\u0103, prezent\u0103 de la na\u0219tere, care afecteaz\u0103 capacitatea s\u00e2ngelui de a se coagula. Ea apare din cauza lipsei sau func\u021bion\u0103rii defectuoase a unor factori de coagulare \u2014 cel mai frecvent factorul VIII (hemofilia A) sau factorul IX (hemofilia B).<\/p>\n<p>Boala este, de regul\u0103, mo\u0219tenit\u0103 de la mam\u0103 \u0219i afecteaz\u0103 \u00een principal b\u0103ie\u021bii. \u00cen aproximativ 30% dintre cazuri, apare \u00eens\u0103 spontan, f\u0103r\u0103 antecedente familiale. De\u0219i femeile sunt, de obicei, purt\u0103toare, unele pot prezenta forme u\u0219oare de s\u00e2ngerare.<\/p>\n<p><strong>Cum se manifest\u0103?<\/strong><\/p>\n<p>Semnul principal al hemofiliei este s\u00e2ngerarea prelungit\u0103 \u0219i dificil de oprit. Aceasta poate ap\u0103rea:<\/p>\n<ul>\n<li>dup\u0103 lovituri minore sau c\u0103z\u0103turi<\/li>\n<li>la nivelul articula\u021biilor, provoc\u00e2nd durere, inflama\u021bie \u0219i limitarea mi\u0219c\u0103rii<\/li>\n<li>la nivel muscular sau intern<\/li>\n<li>dup\u0103 interven\u021bii medicale sau extrac\u021bii dentare<\/li>\n<\/ul>\n<p>\u00cen mod normal, organismul formeaz\u0103 un cheag de s\u00e2nge pentru a opri s\u00e2ngerarea, folosind trombocite \u0219i factori de coagulare. \u00cen hemofilie, acest proces este \u00eent\u00e2rziat sau ineficient.<\/p>\n<p><strong>C\u00e2t de frecvent\u0103 este?<\/strong><\/p>\n<p>Hemofilia afecteaz\u0103 aproximativ 100 de persoane la un milion de locuitori. \u00cen Rom\u00e2nia, sunt \u00een jur de 2.000 de persoane diagnosticate, iar forma A este de 5\u20136 ori mai frecvent\u0103 dec\u00e2t forma B.<\/p>\n<p><strong>Tipuri de hemofilie<\/strong><\/p>\n<ul>\n<li>Hemofilia A \u2013 lipsa factorului VIII<\/li>\n<li>Hemofilia B \u2013 lipsa factorului IX<\/li>\n<li>Hemofilia C \u2013 lipsa factorului XI (mult mai rar\u0103)<\/li>\n<\/ul>\n<p><strong>Forme de severitate<\/strong><\/p>\n<p>\u00cen func\u021bie de cantitatea de factor de coagulare din s\u00e2nge:<\/p>\n<ul>\n<li>form\u0103 sever\u0103: sub 1%<\/li>\n<li>form\u0103 medie: 1\u20134%<\/li>\n<li>form\u0103 u\u0219oar\u0103: 5\u201330%<\/li>\n<\/ul>\n<p>Formele severe sunt de obicei diagnosticate \u00een primii ani de via\u021b\u0103, c\u00e2nd copilul \u00eencepe s\u0103 mearg\u0103 \u0219i apar traumatisme frecvente. Formele u\u0219oare pot fi descoperite mai t\u00e2rziu, uneori doar \u00een urma unei interven\u021bii chirurgicale sau a unui accident.<\/p>\n<p><strong>Tratament<\/strong><\/p>\n<p>Hemofilia este o boal\u0103 cronic\u0103, dar tratabil\u0103. Tratamentul const\u0103 \u00een administrarea factorului de coagulare lips\u0103, fie preventiv (profilactic), fie \u00een situa\u021bii de s\u00e2ngerare.<\/p>\n<p>La Spitalul Jude\u021bean de Urgen\u021b\u0103 Buz\u0103u, tratamentul este asigurat prin Programul Na\u021bional de Hemofilie \u0219i include:<\/p>\n<ul>\n<li>tratament profilactic pentru copii<\/li>\n<li>tratamentul episoadelor de s\u00e2ngerare (la copii \u0219i adul\u021bi)<\/li>\n<li>recuperare medical\u0103 prin kinetoterapie<\/li>\n<\/ul>\n<p>Programul, derulat din 2008, este coordonat de medicul primar pediatru Anica Gina \u0219i se adreseaz\u0103 tuturor pacien\u021bilor, indiferent de v\u00e2rst\u0103.<\/p>\n<p><strong>De ce este important diagnosticul?<\/strong><\/p>\n<p>Hemofilia este o afec\u021biune rar\u0103, dar serioas\u0103, iar simptomele \u2014 v\u00e2n\u0103t\u0103i frecvente, s\u00e2nger\u0103ri prelungite sau dureri articulare \u2014 sunt adesea ignorate, mai ales la copii, sau considerate normale \u00een cazul femeilor.<\/p>\n<p>Accesul la centre specializate r\u0103m\u00e2ne inegal, iar la nivel global peste 75% dintre persoanele afectate nu sunt diagnosticate.<\/p>\n<\/div>\n<p>[analyse_source url=&#8221;https:\/\/blitz24.ro\/national\/astazi-se-sarbatoreste-ziua-internationala-a-hemofiliei\/&#8221;]<\/p>\n","protected":false},"excerpt":{"rendered":"<p>[analyse_image type=&#8221;featured&#8221; src=&#8221;https:\/\/blitz24.ro\/wp-content\/uploads\/2026\/04\/ziua-internationala-a-hemofiliei-scaled.jpg&#8221;] Ziua Interna\u021bional\u0103 a Hemofiliei, s\u0103rb\u0103torit\u0103 ast\u0103zi, 17 aprilie, reprezint\u0103 o oportunitate important\u0103 de a cre\u0219te gradul de informare al popula\u021biei cu privire la diagnosticarea \u0219i tratamentul acestei afec\u021biuni, dar \u0219i de a atrage aten\u021bia autorit\u0103\u021bilor asupra necesit\u0103\u021bii \u00eembun\u0103t\u0103\u021birii accesului la servicii medicale. De\u0219i hemofilia nu se vindec\u0103, tratamentul adecvat permite pacien\u021bilor s\u0103 [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[2],"tags":[42,226],"class_list":["post-1888456","post","type-post","status-publish","format-standard","hentry","category-politics","tag-blitz24-ro","tag-crawlmanager"],"_links":{"self":[{"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=\/wp\/v2\/posts\/1888456","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=1888456"}],"version-history":[{"count":0,"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=\/wp\/v2\/posts\/1888456\/revisions"}],"wp:attachment":[{"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=1888456"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=%2Fwp%2Fv2%2Fcategories&post=1888456"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/analyse.optim.biz\/index.php?rest_route=%2Fwp%2Fv2%2Ftags&post=1888456"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}